Diagnostic criteria for idiopathic pulmonary fibrosis: A Fleischner Society white paper Journal Article


Authors: Lynch, D. A.; Sverzellati, N.; Travis, W. D.; Brown, K. K.; Colby, T. V.; Galvin, J. R.; Goldin, J. G.; Hansell, D. M.; Inoue, Y.; Johkoh, T.; Nicholson, A. G.; Knight, S. L.; Raoof, S.; Richeldi, L.; Ryerson, C. J.; Ryu, J. H.; Wells, A. U.
Article Title: Diagnostic criteria for idiopathic pulmonary fibrosis: A Fleischner Society white paper
Abstract: This Review provides an updated approach to the diagnosis of idiopathic pulmonary fibrosis (IPF), based on a systematic search of the medical literature and the expert opinion of members of the Fleischner Society. A checklist is provided for the clinical evaluation of patients with suspected usual interstitial pneumonia (UIP). The role of CT is expanded to permit diagnosis of IPF without surgical lung biopsy in select cases when CT shows a probable UIP pattern. Additional investigations, including surgical lung biopsy, should be considered in patients with either clinical or CT findings that are indeterminate for IPF. A multidisciplinary approach is particularly important when deciding to perform additional diagnostic assessments, integrating biopsy results with clinical and CT features, and establishing a working diagnosis of IPF if lung tissue is not available. A working diagnosis of IPF should be reviewed at regular intervals since the diagnosis might change. Criteria are presented to establish confident and working diagnoses of IPF. © 2018 Elsevier Ltd
Keywords: disease course; review; patient selection; pathophysiology; diagnostic procedure; computer assisted tomography; image analysis; clinical assessment; evidence based practice; practice guideline; histology; clinical evaluation; medical literature; fibrosing alveolitis; thorax radiography; genetic disorder; autoimmune disease; medical information system; general practitioner; lung biopsy; lymphadenopathy; drug induced disease; interstitial pneumonia; allergic pneumonitis; lung parenchyma; ground glass opacity; bronchiectasis; systematic review (topic); interdisciplinary research; human; priority journal; honeycombing; occupational lung disease
Journal Title: The Lancet Respiratory Medicine
Volume: 6
Issue: 2
ISSN: 2213-2600
Publisher: Elsevier Inc.  
Date Published: 2018-02-01
Start Page: 138
End Page: 153
Language: English
DOI: 10.1016/s2213-2600(17)30433-2
PROVIDER: scopus
PUBMED: 29154106
DOI/URL:
Notes: Review -- Export Date: 1 March 2018 -- Source: Scopus
Altmetric
Citation Impact
BMJ Impact Analytics
MSK Authors
  1. William D Travis
    743 Travis
Related MSK Work