Zebras and hen's teeth: Recognition and management of rare T and NK lymphomas Journal Article


Authors: Mehta-Shah, N.; Horwitz, S.
Article Title: Zebras and hen's teeth: Recognition and management of rare T and NK lymphomas
Abstract: Although all the peripheral T-cell lymphomas are uncommon, there are some entities that are truly rare. Subtypes, such as enteropathy-associated T-cell lymphoma, hepatosplenic T-cell lymphoma, extranodal NK/T-cell lymphoma, and subcutaneous panniculitis-like T-cell lymphoma, have an approximate annual incidence in United States of <500 each. In these very rare subtypes, there is limited data to guide clinical decision-making. As such, our treatment decisions are often based on extrapolation, case series, personal experience, and biases. We summarize the existing data regarding initial management of these entities and compare how that management follows paradigms established for the more common T-cell lymphomas.
Keywords: chemotherapy; analysis; united-states; high-dose; multicenter; hematopoietic sct; l-asparaginase; gamma-delta; nasal type; killer/t-cell lymphoma; involved-field radiation; stage ie
Journal Title: Hematology-American Society of Hematology Education Program
Volume: 2015
ISSN: 1520-4391
Publisher: American Society of Hematology  
Date Published: 2015-12-05
Start Page: 545
End Page: 549
Language: English
ACCESSION: WOS:000369607000078
PROVIDER: wos
PUBMED: 26637770
DOI: 10.1182/asheducation-2015.1.545
Notes: Article -- Source: Wos
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  1. Steven M Horwitz
    645 Horwitz
  2. Neha Mehta Shah
    23 Shah