Abstract: |
Extraosseous Ewing's sarcoma/primitive neuroectodermal tumor (ES/PNET) is a rare soft tissue tumor of childhood usually found in the extremities. The authors present the case of a 17-year-old girl who presented with right flank pain and hematuria and during operation was found to have a right ureteral mass. The histopathologic, immunohistochemical, ultrastructural, and cytogenetic characteristics of the excised mass were consistent with extraosseous ES/PNET. This is the first known reported case of extraosseous ES/PNET of the ureter. The pathologic features and clinical management of this case, as well as a review of the literature, are presented. Copyright (C) 2000 by W.B. Saunders Company. |
Keywords: |
adolescent; clinical feature; disease course; case report; doxorubicin; cancer combination chemotherapy; combined modality therapy; antineoplastic combined chemotherapy protocols; cyclophosphamide; vincristine; childhood cancer; ewing sarcoma; translocation, genetic; ureteral neoplasms; ureter; sarcoma, ewing's; chromosomes, human, pair 11; neuroectoderm tumor; ureter tumor; primitive neuroectodermal tumor; neuroectodermal tumors, primitive, peripheral; chromosomes, human, pair 22; humans; prognosis; human; female; priority journal; article; extraosseous ewing's sarcoma
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