Dermatofibrosarcoma protuberans, version 1.2014 Journal Article


Authors: Bichakjian, C. K.; Olencki, T.; Alam, M.; Andersen, J. S.; Berg, D.; Bowen, G. M.; Cheney, R. T.; Daniels, G. A.; Glass, L. F.; Grekin, R. C.; Grossman, K.; Ho, A. L.; Lewis, K. D.; Lydiatt, D. D.; Morrison, W. H.; Nehal, K. S.; Nelson, K. C.; Nghiem, P.; Perlis, C. S.; Shaha, A. R.; Thorstad, W. L.; Tuli, M.; Urist, M. M.; Wang, T. S.; Werchniak, A. E.; Wong, S. L.; Zic, J. A.; McMillian, N.; Hoffman, K.; Ho, M.
Article Title: Dermatofibrosarcoma protuberans, version 1.2014
Abstract: Dermatofibrosarcoma protuberans (DFSP) is an uncommon soft tissue tumor characterized by a relatively high risk of local recurrence and low risk of metastasis. The NCCN Guidelines for DFSP provide multidisciplinary recommendations on the management of patients with this rare disease. These NCCN Guidelines Insights highlight the addition of the Principles of Pathology section, which provides recommendations on the pathologic assessment of DFSP. Because DFSP can mimic other lesions, immunohistochemical studies are often required to establish diagnosis. Cytogenetic testing for the characteristic translocation t(17;22)(q22;q13) can also be valuable in the differential diagnosis of DFSP with other histologically similar tumors. © JNCCN-Journal of the National Comprehensive Cancer Network.
Journal Title: Journal of the National Comprehensive Cancer Network
Volume: 12
Issue: 6
ISSN: 1540-1405
Publisher: Harborside Press  
Date Published: 2014-06-01
Start Page: 863
End Page: 868
Language: English
PROVIDER: scopus
PUBMED: 24925197
DOI/URL:
Notes: JNCCN J. Nat. Compr. Cancer Netw. -- Export Date: 8 July 2014 -- Source: Scopus
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MSK Authors
  1. Ashok R Shaha
    699 Shaha
  2. Kishwer S Nehal
    279 Nehal
  3. Alan Loh Ho
    240 Ho
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