Cystic lung disease and Birt-Hogg-DubÉ Syndrome: Diagnosis and management Journal Article
| Authors: | Bures, S.; White, D. A. |
| Article Title: | Cystic lung disease and Birt-Hogg-DubÉ Syndrome: Diagnosis and management |
| Abstract: | Birt-Hogg-DubÉ (BHD) is a familial syndrome that leads to the development of lung cysts and carries a significantly increased risk of spontaneous pneumothorax. Other manifestations are benign hair follicle tumors and a high incidence of renal cancers. The diagnosis is often first considered when unexplained lung cysts are found. Recognition of the syndrome by chest physicians is important because of the risk of spontaneous pneumothorax and because BHD patients and families require screening for renal cancers. Clinical features of BHD are given as well as recommendations for management of patients with BHD and their families. Copyright © Lippincott Williams & Wilkins. |
| Keywords: | adult; clinical feature; case report; computer assisted tomography; risk assessment; pneumothorax; needle biopsy; physician; physical examination; birt hogg dube syndrome; kidney cancer; birthoggdubé; lung cysts; pneumothorax renal tumors; lung cyst; trichilemmoma |
| Journal Title: | Clinical Pulmonary Medicine |
| Volume: | 15 |
| Issue: | 4 |
| ISSN: | 1068-0640 |
| Publisher: | Lippincott Williams & Wilkins |
| Date Published: | 2008-07-01 |
| Start Page: | 235 |
| End Page: | 237 |
| Language: | English |
| DOI: | 10.1097/CPM.0b013e31817dfc4d |
| PROVIDER: | scopus |
| DOI/URL: | |
| Notes: | --- - "Export Date: 17 November 2011" - "CODEN: CPMEF" - "Source: Scopus" |
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