Neuroblastoma and other adrenal tumors Book Section


Authors: Christison-Lagay, E. R.; La Quaglia, M. P.
Editors: Carachi, R.; Grosfeld , J. L.
Article/Chapter Title: Neuroblastoma and other adrenal tumors
Abstract: This chapter addresses the medical presentation, histology, biological features, risk stratification, and surgical management of malignant adrenal disease. Neuroblastoma is the most common adrenal neoplasm in the pediatric population, accounting for 97 % of adrenal neoplasms in children younger than 15 months. It is 50 times more common than pheochromocytoma, the next most common tumor. The good prognosis associated with early-stage, biologically favorable disease, with a survival rate of more than 90 %, stands in dramatic contradistinction to the poor prognosis associated with metastatic or biologically unfavorable presentations. Treatment is typically determined by the risk stratification schemes of the Children’s Oncology Group, the International Neuroblastoma Staging System, and the International Neuroblastoma Research Group. © Springer-Verlag Berlin Heidelberg 2016.
Keywords: neuroblastoma; pheochromocytoma; adrenocortical carcinoma; adrenal tumors; adrenal adenoma; adrenal calcification; aldosteronoma
Book Title: The Surgery of Childhood Tumors. 3rd ed
ISBN: 978-3-662-48588-0
Publisher: Springer Berlin Heidelberg  
Publication Place: London, UK
Date Published: 2016-01-01
Start Page: 231
End Page: 256
Language: English
DOI: 10.1007/978-3-662-48590-3_14
PROVIDER: scopus
DOI/URL:
Notes: Book Chapter -- Export Date: 2 August 2016 -- Source: Scopus
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