Clear cell sarcoma of the stomach Journal Article


Authors: Lagmay, J. P.; Ranalli, M.; Arcila, M.; Baker, P.
Article Title: Clear cell sarcoma of the stomach
Abstract: Clear cell sarcoma (CCS) is a high grade soft tissue sarcoma with a distinct molecular profile. Gastrointestinal CCS is very rare and most reported cases are in adults. We describe a 10-year-old female with a 4-month history of anemia who later developed fever, weight loss and abdominal pain. She was subsequently found to have a large infiltrative gastric mass. A diagnosis of CCS was confirmed by molecular and cytogenetic studies. This case illustrates the necessity of a multimodal approach, particularly the use of molecular studies, in the diagnostic evaluation of rare tumors presenting in unusual sites. © 2009 Wiley-Liss, Inc.
Keywords: immunohistochemistry; cancer chemotherapy; child; school child; oncoprotein; genetics; case report; doxorubicin; multimodality cancer therapy; combined modality therapy; lymph node metastasis; antineoplastic agent; in situ hybridization, fluorescence; reverse transcription polymerase chain reaction; computer assisted tomography; multiple cycle treatment; anemia; tumor volume; vomiting; antineoplastic combined chemotherapy protocols; radiotherapy; weight reduction; transcription factor; cytogenetics; pathology; histology; ifosfamide; pediatric; transcription factors; abdominal pain; fever; liver metastasis; fluorescence in situ hybridization; reverse transcriptase polymerase chain reaction; oncogene proteins, fusion; gastrectomy; chromosome analysis; stomach neoplasms; stomach tumor; clear cell sarcoma of soft tissues; ews-atf1; gastrointestinal clear cell sarcoma; visceral clear cell sarcoma; ferritin; ews atf1 fusion protein, human; ews-atf1 fusion protein, human; clear cell sarcoma; erythrocyte sedimentation rate; rna extraction; satiety; stomach sarcoma; thrombocytosis; sarcoma, clear cell
Journal Title: Pediatric Blood and Cancer
Volume: 53
Issue: 2
ISSN: 1545-5009
Publisher: Wiley Periodicals, Inc  
Date Published: 2009-08-01
Start Page: 214
End Page: 216
Language: English
DOI: 10.1002/pbc.22014
PUBMED: 19350639
PROVIDER: scopus
DOI/URL:
Notes: --- - "Export Date: 30 November 2010" - "CODEN: PBCEA" - "Source: Scopus"
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  1. Maria Eugenia Arcila
    657 Arcila