Niemann-Pick Disease versus acid sphingomyelinase deficiency Journal Article


Authors: Lozano, J.; Morales, A.; Cremesti, A.; Fuks, Z.; Tilly, J. L.; Schuchman, E.; Gulbins, E.; Kolesnick, R.
Article Title: Niemann-Pick Disease versus acid sphingomyelinase deficiency
Keywords: signal transduction; controlled study; clinical feature; disease classification; nonhuman; letter; t lymphocyte; animal cell; mouse; phenotype; animals; mice; mice, knockout; cells, cultured; apoptosis; spleen; animal model; enzyme activity; b lymphocyte; animalia; liver; disease severity; cell transformation; fibroblasts; liver cell; point mutation; tremor; lipid metabolism; hydrolysis; degenerative disease; epstein barr virus; ceramide; ceramides; spleen cell; sphingomyelin phosphodiesterase; ovary development; adulthood; radiation tolerance; sphingomyelin; second messenger; human herpesvirus 4; niemann pick disease; niemann-pick diseases; infancy; caveolin 1; humans; female; priority journal; membrane damage; caveolins
Journal Title: Cell Death and Differentiation
Volume: 8
Issue: 1
ISSN: 1350-9047
Publisher: Nature Publishing Group  
Date Published: 2001-01-01
Start Page: 100
End Page: 102
Language: English
DOI: 10.1038/sj.cdd.4400775
PUBMED: 11313707
PROVIDER: scopus
DOI/URL:
Notes: Export Date: 21 May 2015 -- Source: Scopus
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  1. Zvi Fuks
    427 Fuks
  2. Jose Lozano
    8 Lozano
  3. Richard N Kolesnick
    299 Kolesnick