Authors: | Oppenheimer, O.; Athanasian, E.; Meyers, P.; Antonescu, C. R.; Gorlick, R. |
Article Title: | Malignant ectomesenchymoma in the wrist of a child: Case report and review of the literature |
Abstract: | Malignant ectomesenchymomas, rare and potentially aggressive tumors, occur in children and exhibit mesenchymal and neuroectodermal components. This report describes the first patient diagnosed with a malignant ectomesenchymoma of the hand. The patient was a 17-month-old male who developed a hypothenar mass on his left hand that was surgically excised. Microscopic evaluation revealed ganglioneuroblastic, rhabdomyosarcomatous, and chondrosarcomatous elements. Following excisional biopsy he was treated with cyclophosphamide, doxorubicin, vincristine, ifosfamide, and etoposide. After 3 courses of chemotherapy the patient had a wide reexcision with no residual tumor. The patient is 4 years from diagnosis, without evidence of disease. |
Keywords: | disease-free survival; cancer surgery; histopathology; review; microscopy; case report; doxorubicin; cancer combination chemotherapy; chemotherapy; etoposide; antineoplastic combined chemotherapy protocols; cyclophosphamide; vincristine; tumor biopsy; ifosfamide; infant; neuroblastoma; reoperation; malignant neoplastic disease; rhabdomyosarcoma; chondrosarcoma; neuroectoderm tumor; pediatric tumors; soft tissue neoplasms; hand; wrist; mesenchymoma; malignant ectomesenchymoma |
Journal Title: | International Journal of Surgical Pathology |
Volume: | 13 |
Issue: | 1 |
ISSN: | 1066-8969 |
Publisher: | Sage Publications |
Date Published: | 2005-01-01 |
Start Page: | 113 |
End Page: | 116 |
Language: | English |
PUBMED: | 15735865 |
PROVIDER: | scopus |
DOI/URL: | |
Notes: | --- - "Cited By (since 1996): 3" - "Export Date: 24 October 2012" - "CODEN: IJSPF" - "Source: Scopus" |