Authors: | Roggin, K. K.; Rudloff, U.; Klimstra, D. S.; Russell, L. A.; Blumgart, L. H. |
Article Title: | Adult-onset asthma and periocular xanthogranulomas in a patient with lymphoplasmacytic sclerosing pancreatitis |
Abstract: | The clinical syndrome of adult-onset asthma and periocular xanthogranulomas represents a rare systemic autoimmune disorder that has not been previously associated with autoimmune pancreatitis. Herein, we describe the case report of a 61-year-old man with the unique clinical association of adult-onset asthma, atopy, and periocular xanthogranulomas, who had previously been diagnosed with lymphoplasmacytic sclerosing pancreatitis. We have previously reported the case of a patient with lymphoplasmacytic sclerosing pancreatitis that developed postoperative inflammatory pseudotumor of the orbit. These unique, extrapancreatic, ocular manifestations of this disease add to the published observations that it is a systemic disorder with the potential for multiorgan involvement that may have a spectrum of clinical manifestations that includes adult-onset asthma and periocular xanthogranulomas. © 2007 Lippincott Williams & Wilkins, Inc. |
Keywords: | adult; human tissue; middle aged; human cell; clinical feature; anamnesis; case report; disease association; pancreatitis; asthma; eye disease; autoimmune diseases; onset age; age of onset; plasma cells; sclerosis; xanthogranuloma; multiple organ failure; histiocytes; granuloma, plasma cell; autoimmune pancreatitis; lymphoplasmacytic sclerosing pancreatitis; systemic disease; orbit; aapox; ocular lesions; eye xanthogranuloma; orbit pseudotumor; postoperative inflammation; orbital diseases; xanthomatosis |
Journal Title: | Pancreas |
Volume: | 34 |
Issue: | 1 |
ISSN: | 0885-3177 |
Publisher: | Lippincott Williams & Wilkins |
Date Published: | 2007-01-01 |
Start Page: | 157 |
End Page: | 160 |
Language: | English |
DOI: | 10.1097/01.mpa.0000236737.84982.45 |
PUBMED: | 17198199 |
PROVIDER: | scopus |
DOI/URL: | |
Notes: | --- - "Cited By (since 1996): 6" - "Export Date: 17 November 2011" - "CODEN: PANCE" - "Source: Scopus" |